9,887 annual reviews were recorded in 2017, 192 more than 2016.
20 is the median age of people with CF on the Registry. 60.6% of people on the Registry are aged 16 or over.
33.6% of people under 16, and 52.4% of people 16 and over, had IV antibiotics in 2017. The median number of days spent on IVs was 16 for children, and 28 for adults aged 16 and over.
Burden of treatment
20% of people with cystic fibrosis take three or more inhaled medications.
Median predicted survival
Median predicted survival for people born today, using 2013-2017 data, is 47 years old. The median predicted survival for females (43.1) is 6.5 years lower than males (49.6).
58 women with cystic fibrosis had babies in 2017.
44 men with cystic fibrosis became fathers in 2017.
People with CF taking cystic fibrosis related diabetes (CFRD) treatment:
12.2% of children, aged 10-15
33.8% of adults, aged 16
People with CF who have been screened for CFRD:
24.7% have an existing CFRD diagnosis
19.3% have not been screened
51 adults received a lung transplant, compared to 46 in 2016.
235 people with CF were evaluated for transplant in 2017, and 121 were accepted onto a transplant waiting list.
Route to diagnosis
7247 (73.3%) of people on the Registry were diagnosed through methods other than newborn screening. The most common of these are:
- Abnormal stools/fatty stool (steatorrhea)/malabsorption
- Persistent or acute respiratory infection
- Failure to thrive/malnutrition